Jan 5, 2024 · Following a low-phenylalanine diet can prevent intellectual disability and other complications in people with phenylketonuria. The diet focuses on low protein foods and avoids high protein...

Dec 8, 2023 · This article discusses which foods people with PKU should include or avoid in a phenylketonuria diet. It also discusses when to speak with a doctor about a PKU diet.

Jul 12, 2023 · A PKU diet typically includes a phenylalanine-free medical formula or shake to meet your daily nutritional needs along with carefully measured amounts of fruits, vegetables, breads, pasta, and cereals to ensure you obtain just the …

What is a low phenylalanine diet? A low phenylalanine diet is the main treatment for phenylketonuria (PKU). People with PKU must restrict phenylalanine which is found in protein. However, phenylalanine cannot be removed completely, so it is given in measured exchange amounts each day. What is a protein (PKU) exchange?

The diet for PKU consists of a phenylalanine-free medical formula and carefully measured amounts of fruits, vegetables, bread, pasta, and cereals. Many people who follow a low phenylalanine (phe) food pattern eat special low protein breads and pastas.

A strict, lifelong low phenylalanine diet is the principle treatment in PKU. It may be the only treatment or used in combination with drug treatments. This diet manual describes the practical application of the European PKU guidelines .

Apr 24, 2017 · Phenylketonuria, or PKU, is a genetically inherited birth defect that causes an unwanted buildup of the amino acid phenylalanine in the blood, and a strict diet limited in phenylalanine is the main treatment.

The PKU diet regime is a low phenylalanine diet, ie very low in protein containing foods, and when the phenylalanine content of food is known a phe exchange value is allocated, otherwise, protein values are used, which can mean interpreting the label on manufactured foods.

The purpose of these guidelines is to present an organized way to start and maintain a phenylalanine (PHE)-restricted diet for a previously untreated adult with phenylketonuria (PKU).

Phenylketonuria (PKU) is a rare but potentially serious inherited disorder. Our bodies break down the protein in foods, such as meat and fish, into amino acids, which are the "building blocks" of protein. These amino acids are then used to make our own proteins. Any amino acids that are not needed are broken down further and removed from the body.